Bilateral Neurolymphomatosis of the Cerebellopontine Angle
DOI:
https://doi.org/10.46531/sinapse/CC/230056/2023Keywords:
Cerebellar Neoplasms, Cerebellopontine Angle, LymphomaAbstract
Tumours of the cerebellopontine angle and internal auditory canal are frequent, typically vestibular schwannomas (only rarely bilateral) and meningiomas. We describe the case of a 76-year-old man who presented with persistent peripheral facial paralysis, which proved to be secondary to a process of bilateral primary neurolymphomatosis of the facial and vestibulocochlear cranial nerves, caused by sequential involvement of both cerebellopontine angles and internal auditory canals due to diffuse large B-cell lymphoma. Neurolymphomatosis is an uncommon cause of lesions with this topography. Its diagnosis is usually difficult and time-consuming, and the prognosis ominous. Nevertheless, and in face of the possibility of a good response to targeted treatment, if promptly initiated, this entity should be taken into account in the differential diagnosis of tumours of the cerebellopontine angle in patients with atypical or aggressive progression.Downloads
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