Idiopathic Orbital Myositis in the Pediatric Age Group: A Rare Cause of Ocular Pain – Case Report
DOI:
https://doi.org/10.46531/sinapse/CC/193/2026Keywords:
Child, Oculomotor Muscles, Orbital Myositis/diagnostic imaging, Orbital Myositis/drug therapyAbstract
Idiopathic orbital myositis is a rare clinical entity in pediatric age, with its pathophysiology not yet fully understood. Patients typically present with unilateral ocular complaints such as pain aggravated by eye movements, erythema and eyelid edema, chemosis, and conjunctival hyperemia. Magnetic resonance imaging plays a crucial role in identifying the affected muscles. We report the case of a 14-year-old adolescent who presented with right ocular pain, aggravated by eye movements, for one month. Upon suspicion of an inflammatory or infectious process in the right orbital region, magnetic resonance imaging was performed, revealing thickening of the lateral rectus muscle in the right orbit. The diagnosis of idiopathic orbital myositis was established, and treatment with prednisolone was initiated, resulting in complete resolution of the clinical symptoms. The description of this case aims to raise awareness of this condition in the pediatric age group.
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Harris GJ. Idiopathic orbital inflammation: a pathogenetic construct and treatment strategy: The 2005 ASOPRS Foundation Lecture. Ophthalmic Plastic and Reconstructive Surgery. 2006; 22:79-86. doi:10.1097/01.iop.0000203734.52333.93
Yan J, Qiu H, Wu Z, Li Y. Idiopathic orbital inflammatory pseudotumor in Chinese children. Orbit. 2006;25:1-4. doi: 10.1080/01676830500505608
Li Z, Chen Y, Liu H, Wu Q, Yang B, Zhang J, et al. Clinical features and recurrence patterns of pediatric idiopathic orbital inflammatory disease. BMC Ophthalmol. 2025;25:649. doi:10.1186/s12886-025-04498-7.
Mombaerts I, McNab AA. Idiopathic Orbital Myositis Revisited. Curr Rheumatol Rep. 2022;24:20-26. doi: 10.1007/s11926-022-01052-y
Fang Y, Shen B, Dai Q, Xie Q, Wu W, Wang M. Orbital inflammatory pseudotumor: new advances in diagnosis, pathogenesis, and treatment. Eur J Med Res. 2023;28:395. doi:10.1186/s40001-023-01330-0
Tanya SM, Kulbay M, Fonseca Falcao M. Orbital myositis: a rare initial manifestation of pediatric Crohn's disease. Can J Ophthalmol. 2025;60:e646-e648. doi:10.1016/j.jcjo.2025.03.011
Mahdaviani S, Higgins, G, Kerr, N. Orbital pseudotumor in a child with juvenile rheumatoid arthritis. J Pediatr Ophthalmol Strabismus. 2005;42;185-8.
Montagnese F, Wenninger S, Schoser B. "Orbiting around" the orbital myositis: clinical features, differential diagnosis and therapy. J Neurol. 2016;263:631-40. doi: 10.1007/s00415-015-7926-x
Parra-Rodas LM, Parra-Rodas E, Jimenez-Villegas MJ, Cartagena-Agudelo Y, Cabrera-Hemer DN. Miositis orbitaria, una causa de oftalmoplejia dolorosa en pediatria. Rev Chil Pediatr. 2020;91:930-5. doi: 10.32641/rchped.v91i6.1484
Spindle J, Tang SX, Davies B, Wladis EJ, Piozzi E, Pellegrini M, et al. Pediatric Idiopathic Orbital Inflammation: Clinical Features of 30 Cases. Ophthalmic Plast Reconstr Surg. 2016;32:270-4. doi:10.1097/IOP.0000000000000494
Kang MS, Yang HK, Kim N, Hwang JM. Clinical Features of Ocular Motility in Idiopathic Orbital Myositis. J Clin Med. 2020;9:1165. doi: 10.3390/jcm9041165.
Culligan B. Orbital myositis following streptococcal pharyngitis in a pediatric patient. Optometry. 2005;76:250-8. doi:10.1016/s1529-1839(05)70300-6.
Pakdaman MN, Sepahdari AR, Elkhamary SM. Orbital inflammatory disease: pictorial review and differential diagnosis. World J Radiol. 2014;6:106-15. doi:10.4329/wjr.v6.i4.106.
Ota M, Shimizu T, Yoshida H, Kawata A, Kinoshita M, Nakano S, et al. Clinical features and therapeutic responses of idiopathic orbital myositis. Neurol Clin Neurosci. 2015;3:63-67. doi: 10.1111/ncn3.151
Eshraghi B, Sonbolestan SA, Abtahi MA, Mirmohammadsideghi A. Clinical characteristics, histopathology, and treatment outcomes in adult and pediatric patients with nonspecific orbital inflammation. J Curr Ophthalmol. 2019;31:327-34. doi:10.1016/j.joco.2019.03.004
Keen JA, Kennedy BJ, Mishulin A, Winkler K, Fernandez-Ruiz M, Black EH, Roarty J. Adult Versus Pediatric Relapse and Recurrence in Orbital Inflammatory Syndrome. Ophthalmic Plast Reconstr Surg. 2021;37:77-80. doi: 10.1097/IOP.0000000000001705.
Wiersinga WM, Regensburg NI, Mourits MP. Differential involvement of orbital fat and extraocular muscles in Graves' ophthalmopathy. Eur Thyroid J. 2013;2:14-21. doi:10.1159/000348246
Keen S, Lapira M, McCallum E, Sipkova Z, Qureshi A, Wilson S, et al. Paediatric orbital lymphoma; a case series and review of the literature. Eye. 2023;37:1013-9. doi:10.1038/s41433-022-02253-y
Agarwal A, Vempuluru VS, Kaliki S. Primary ocular, adnexal, and orbital rhabdomyosarcoma: A review. Surv Ophthalmol. 2025;70:868-81. doi:10.1016/j.survophthal.2025.03.009
Porhajihosseini S, Al-Sallami A, Al-Rubaye S. Idiopathic lateral rectus myositis in preteens: a case report. Radiol Case Rep. 2022;17:4580-3. doi:10.1016/j.radcr.2022.08.109.
Hattori H, Ohnishi S, Nakagawa Y, Ikemiya M, Yamato K, Matsuoka O, et al. An infant with idiopathic orbital myositis poorly responsive to steroid therapy: a case report. Brain Dev. 2005;27:160-2. doi: 10.1016/j.braindev.2004.05.002
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Copyright (c) 2026 Inês Melo, Cláudia Fernandes, Jorge Rodrigues, Lígia M. Ferreira, Filipe Palavra

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